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Haemophagocytic Lymphohistiocytosis (HLH) in a case of Enteric Fever

Vineeta Pande, Agarkhedkar S. R., Ayank Tandon*, Aditya Agarwal

Abstract


HLH is an uncommon, life threatening clinical syndrome cause by a severe hyper inflammatory reaction triggered by an infectious agent. The characteristic symptoms of HLH are due to the persistent stimulation of lymphocytes and histiocytes, leading to hyper-cytokinemia. We report a case of HLH in enteric fever in a13 year old female presenting with fever, lymphadenopathy and pancytopenia due an infection caused by Salmonella.

Keywords


Post infective fever, Organomegly, cytopenias, Hyper ferritinemias.

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References


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DOI: http://dx.doi.org/10.21746/ijbio.2016.03.007

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