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Haemophagocytic Lymphohistiocytosis (HLH) in a case of Enteric Fever

Vineeta Pande, Agarkhedkar S. R., Ayank Tandon*, Aditya Agarwal


HLH is an uncommon, life threatening clinical syndrome cause by a severe hyper inflammatory reaction triggered by an infectious agent. The characteristic symptoms of HLH are due to the persistent stimulation of lymphocytes and histiocytes, leading to hyper-cytokinemia. We report a case of HLH in enteric fever in a13 year old female presenting with fever, lymphadenopathy and pancytopenia due an infection caused by Salmonella.


Post infective fever, Organomegly, cytopenias, Hyper ferritinemias.

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